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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
Chiffres clés
107
Publications avec texte intégral
Open Access
61 %
Mots clés
Effector T cells
Skeletal muscle
Cell therapy
AUTOPHAGY
Xenograft
RNA
Fibrosis
Gene therapy
Intercellular communication
PABPN1
Myosin
Amyotrophic Lateral Sclerosis
Omics
Pharyngeal muscle
Dysferlinopathy
Myoblast
Agrégats de PABPN1
Muscle dystrophy
Aggregate
MAINTENANCE
Secreted vesicles
Anti-acetylcholine receptor antibodies
OPMD
Cross-bridge kinetics
Muscular dystrophy
Aav-U7
AChR antibodies
Regeneration
DUX4
SATELLITE CELLS
Transcriptomics
ALS
MYOPATHY
Functional genomics
Thérapie génique
Neuromuscular disease
Geriatric assessment
Ageing
Regulatory T cells
Aged
APOPTOSIS
Muscle strength
Myopathy
Alphavirus
Biomarker
Satellite cell
Gene replacement
Pax7
PABPN1 agregates
Regenerative medicine
Triplet expansion disease
Myogenesis
Calcium
ARN
GENE
Metabolism
AAV
Nuclear envelope
NICHE
Inflammation
Myopathies
MND
Oculopharyngeal muscular dystrophy
FAPs
FSHD
MUTATIONS
Dystrophie musculaire oculopharyngée
Actin
Human
Dystrophin
Andermann syndrome
Sarcopenia
Neuromuscular junction NMJ
Myositis
Muscle stem cells
DNA methylation
Differentiation
AAV vectors
Epigenetics
2-D PAGE
QUIESCENCE
Satellite cells
Lamins
Accelerometry
Annexin A2
Exon-skipping
Muscle
Myotube
Akt
MEGF10
Muscle fibrosis
Dysferlin
Haploinsufficiency
Duchenne muscular dystrophy
Sporadic ALS
Mass spectrometry
Adipose tissue
Alzheimer's disease
DMD
Myoblasts